• 1.首都醫(yī)科大學(xué)附屬復(fù)興醫(yī)院血管外科(北京 100038);;
  • 2.首都醫(yī)科大學(xué)附屬宣武醫(yī)院血管外科(北京 100053);

目的 探討布-加綜合征的個體化治療。 方法 我們對首都醫(yī)科大學(xué)附屬復(fù)興醫(yī)院及宣武醫(yī)院、二炮總醫(yī)院及其他醫(yī)院2004年2月至2009年5月期間會診收治的20例布-加綜合征患者的臨床資料進行回顧性分析。結(jié)果 20例患者中術(shù)后24 h死亡1例(5.0%),死于DIC; 19例順利出院。19例患者術(shù)后均獲隨訪,隨訪時間(34.7±3.3)個月,其中恢復(fù)良好者占73.7%(14/19); 1例(5.3%)行腸-腔-頸轉(zhuǎn)流術(shù)者,術(shù)后間斷出現(xiàn)肝性腦病,短期住院治療后可以改善; 術(shù)后18個月1例(5.3%)行腸-腔轉(zhuǎn)流術(shù)者因全身臟器衰竭死亡。結(jié)論 個體化手術(shù)治療方案可明顯提高布-加綜合征患者的生存率。

引用本文: 李春民,卞策,汪忠鎬. 布-加綜合征的個體化手術(shù)治療. 中國普外基礎(chǔ)與臨床雜志, 2010, 17(12): 1306-1307. doi: 復(fù)制

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2. Wang ZG, Zhu Y, Wang SH, et al. Recognition and management of Budd-Chiari syndrome: report of one hundred cases [J]. J Vasc Surg, 1989; 10(2): 149-156.
3. Wang ZG. Etiology, pathophysiology, and treatment of Budd-Chiari syndrome [A]. In: Chang JB, Olsen ER, Prasad K, et al. Textbook of Angiology [M]. New York: Springer, 2000: 971-978.
4. Wang ZG. Management of Budd-Chiari syndrome: Experience from 430 cases [J]. Asian J Surg, 1996; 19(1): 23-30.
5. Slakey DP, Klein AS, Venbrux AC, et al. Budd-Chiari syndrome: current management options [J]. Ann Surg, 2001; 233(4): 522-527.
6. Klein AS. Management of Budd-Chiari syndrome [J]. Liver Transpl, 2006; 12(11 Suppl 2): S23-S28.
7. Valla DC. Primary Budd-Chiari syndrome [J]. J Hepatol, 2009; 50(1): 195-203.
8. Darwish Murad S, Plessier A, Hernandez-Guerra M, et al. Etiology, management, and outcome of the Budd-Chiari syndrome [J]. Ann Intern Med, 2009; 151(3): 167-175.
9. Plessier A, Valla DC. Budd-Chiari syndrome [J]. Semin Liver Dis, 2008; 28(3): 259-269.
10. Li CM, Wang ZG, Gu YQ, et al. Management of complex patients with Budd-Chiari syndrome [J]. Ann Vasc Surg, 2010; 24(3): 301-307.
11. 陳學(xué)明, 汪忠鎬, 尹振明, 等. 布加綜合征452例術(shù)后并發(fā)癥的處理 [J]. 中華普通外科雜志, 1999; 14(6): 417-420.
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13. 汪忠鎬, 馬頌章, 王仕華, 等. 布加綜合征根治性矯正術(shù)式的探討 [J]. 中華胸心血管外科雜志, 1995; 11(3): 132-134.
14. Wang ZG, Zhang FJ, Meng QY, et al. Evolution on management of hepatocaval syndrome: a team view from 2 654 patients [J]. NAZ J Surg, 2005; 75(1-2): 55-63.
15. 汪忠鎬, 李震. 我國血管外科的現(xiàn)狀和發(fā)展 [J]. 中國普外基礎(chǔ)與臨床雜志, 2006; 13(6): 625-628.
  1. 1. Wang ZG, Jone RS. Budd-Chiari syndrome [J]. Curr Probl Surg, 1996; 33(2): 83-211.
  2. 2. Wang ZG, Zhu Y, Wang SH, et al. Recognition and management of Budd-Chiari syndrome: report of one hundred cases [J]. J Vasc Surg, 1989; 10(2): 149-156.
  3. 3. Wang ZG. Etiology, pathophysiology, and treatment of Budd-Chiari syndrome [A]. In: Chang JB, Olsen ER, Prasad K, et al. Textbook of Angiology [M]. New York: Springer, 2000: 971-978.
  4. 4. Wang ZG. Management of Budd-Chiari syndrome: Experience from 430 cases [J]. Asian J Surg, 1996; 19(1): 23-30.
  5. 5. Slakey DP, Klein AS, Venbrux AC, et al. Budd-Chiari syndrome: current management options [J]. Ann Surg, 2001; 233(4): 522-527.
  6. 6. Klein AS. Management of Budd-Chiari syndrome [J]. Liver Transpl, 2006; 12(11 Suppl 2): S23-S28.
  7. 7. Valla DC. Primary Budd-Chiari syndrome [J]. J Hepatol, 2009; 50(1): 195-203.
  8. 8. Darwish Murad S, Plessier A, Hernandez-Guerra M, et al. Etiology, management, and outcome of the Budd-Chiari syndrome [J]. Ann Intern Med, 2009; 151(3): 167-175.
  9. 9. Plessier A, Valla DC. Budd-Chiari syndrome [J]. Semin Liver Dis, 2008; 28(3): 259-269.
  10. 10. Li CM, Wang ZG, Gu YQ, et al. Management of complex patients with Budd-Chiari syndrome [J]. Ann Vasc Surg, 2010; 24(3): 301-307.
  11. 11. 陳學(xué)明, 汪忠鎬, 尹振明, 等. 布加綜合征452例術(shù)后并發(fā)癥的處理 [J]. 中華普通外科雜志, 1999; 14(6): 417-420.
  12. 12. 汪忠鎬, 王仕華, 吳繼東, 等. 腸系膜靜脈與頸靜脈轉(zhuǎn)流術(shù)治療重型布加綜合征 [J]. 中華外科雜志, 1994; 32(10): 611-613.
  13. 13. 汪忠鎬, 馬頌章, 王仕華, 等. 布加綜合征根治性矯正術(shù)式的探討 [J]. 中華胸心血管外科雜志, 1995; 11(3): 132-134.
  14. 14. Wang ZG, Zhang FJ, Meng QY, et al. Evolution on management of hepatocaval syndrome: a team view from 2 654 patients [J]. NAZ J Surg, 2005; 75(1-2): 55-63.
  15. 15. 汪忠鎬, 李震. 我國血管外科的現(xiàn)狀和發(fā)展 [J]. 中國普外基礎(chǔ)與臨床雜志, 2006; 13(6): 625-628.