• 浙江省麗水學(xué)院醫(yī)學(xué)部外科教研室(麗水323000);

目的總結(jié)黑斑息肉綜合征的外科治療經(jīng)驗(yàn)。方法回顧性分析我院 1986~2002年期間收治的8例黑斑息肉綜合征患者的臨床資料。結(jié)果8例中行部分小腸切除(其余段小腸多處切開,切除息肉)5例; 胃大部切除術(shù)2例; 右半結(jié)腸切除術(shù)1例。本組1例腸套疊致腸壞死急診行腸切除,術(shù)后2年,因小腸息肉引起腸套疊致腸壞死,再次手術(shù)切除壞死腸段; 1例術(shù)后內(nèi)鏡隨訪中發(fā)現(xiàn)直腸息肉,給予內(nèi)鏡下電灼切除; 其余6例未見復(fù)發(fā)。結(jié)論黑斑息肉綜合征手術(shù)主要是針對(duì)胃腸道息肉的治療,解除臨床癥狀; 并注意把握手術(shù)時(shí)機(jī),嚴(yán)格遵循手術(shù)適應(yīng)證,并加強(qiáng)術(shù)后的隨訪。

引用本文: 施勇. 黑斑息肉綜合征的外科治療(附8例報(bào)告). 中國普外基礎(chǔ)與臨床雜志, 2004, 11(4): 356-357. doi: 復(fù)制

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  2. 2. Hemminki A, Markie D, Tomlinson I, et al. A serine/threonine kinase gene defective in PeutzJeghers syndrome [J]. Nature, 1998; 391(6663)∶184.
  3. 3. Jenne DE, Reimann H, Nezu J, et al. PeutzJeghers syndrome is caused by mutations in a novel serine threonine kinase [J]. Nat Genet, 1998; 18(1)∶38.
  4. 4. Edwards DP, Khosraviani K, Stafferton R, et al. Longterm results of polyp clearance by intraoperative enteroscopy in the PeutzJeghers syndrome [J]. Dis Colon Rectum, 2003; 46(1)∶48.