• 貴陽(yáng)醫(yī)學(xué)院外科教研室(貴陽(yáng) 550004);

目的  探討原發(fā)性硬化性膽管炎診斷治療方案。
方法 對(duì)我院外科1972~1998年經(jīng)放射學(xué)檢測(cè)和手術(shù)病理確診的原發(fā)性硬化性膽管炎24例患者進(jìn)行回顧性研究。
結(jié)果  24例中按Thompson分型屬Ⅰ型1例; Ⅱ型5例; Ⅲ型10例; Ⅳ型8例。手術(shù)方法為膽囊切除加T管引流8例; 膽管空腸Roux-en-Y吻合12例; U管支撐引流4例。術(shù)后隨訪2~18年,全組各型總死亡率為25%(6/24)。
結(jié)論  早期診斷和手術(shù)能解決膽汁引流入腸。當(dāng)病變嚴(yán)重、肝功能惡化時(shí),應(yīng)盡早考慮肝移植。

引用本文: 夏亮芳. 原發(fā)性硬化性膽管炎(附24例報(bào)告). 中國(guó)普外基礎(chǔ)與臨床雜志, 2001, 8(2): 81-82下轉(zhuǎn)100. doi: 復(fù)制

1. Thompson HH, Pitt HA, Tomplsins RK, et al. Primary sclerosing cholangitis: A haterogenous disease [J]. Ann Surg, 1982; 196(2)∶127.
2. Lemmer ER, Bornman PC, Krige EJ, et al. Primary sclerosing cholangitis——requiem for biliary drainage operations [J]? Arch Surg,1994; 129(7)∶723.
3. Ismail T, Angrisani L, Powell JE, et al. Primary aclerosing cholangitis:options, prognostic variable and outcome [J]. Surgery, 1991, 78(5):564.
4. Werlin SL, Gilcklich M, Jona J, et al. Sclerosing cholangitis in childhood [J]. J Pediatr, 1980, 96(4)∶433.
5. Myers RH, Cooper JH. Primary sclerosing cholangitis: Complete gross and hietologic recersal after long time steriod therapy [J]. Am J Grastroenterology, 1970; 53(5)∶527.
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7. 黃志強(qiáng)主編.現(xiàn)代腹部外科學(xué) [M].第1版.長(zhǎng)沙:湖南科技出版社,1994:482~483.
8. 夏亮芳.阻塞性黃疸診斷的進(jìn)展[J].普外臨床,1991; 6(1)∶23.
  1. 1. Thompson HH, Pitt HA, Tomplsins RK, et al. Primary sclerosing cholangitis: A haterogenous disease [J]. Ann Surg, 1982; 196(2)∶127.
  2. 2. Lemmer ER, Bornman PC, Krige EJ, et al. Primary sclerosing cholangitis——requiem for biliary drainage operations [J]? Arch Surg,1994; 129(7)∶723.
  3. 3. Ismail T, Angrisani L, Powell JE, et al. Primary aclerosing cholangitis:options, prognostic variable and outcome [J]. Surgery, 1991, 78(5):564.
  4. 4. Werlin SL, Gilcklich M, Jona J, et al. Sclerosing cholangitis in childhood [J]. J Pediatr, 1980, 96(4)∶433.
  5. 5. Myers RH, Cooper JH. Primary sclerosing cholangitis: Complete gross and hietologic recersal after long time steriod therapy [J]. Am J Grastroenterology, 1970; 53(5)∶527.
  6. 6. 傅德良,張延齡.原發(fā)性硬化性膽管炎病例的免疫異常.國(guó)外醫(yī)學(xué)外科學(xué)分冊(cè),1990; 15(3)∶123.
  7. 7. 黃志強(qiáng)主編.現(xiàn)代腹部外科學(xué) [M].第1版.長(zhǎng)沙:湖南科技出版社,1994:482~483.
  8. 8. 夏亮芳.阻塞性黃疸診斷的進(jìn)展[J].普外臨床,1991; 6(1)∶23.